Skip to content

    Cancer Health Center

    Font Size
    A
    A
    A

    Childhood Soft Tissue Sarcoma Treatment (PDQ®): Treatment - Patient Information [NCI] - Treatment Options for Childhood Soft Tissue Sarcoma

    continued...

    Treatment of sclerosing epithelioid fibrosarcoma may include the following:

    • Surgery to completely remove the tumor.

    Skeletal Muscle Tumors

    Rhabdomyosarcoma

    See the PDQ summary on Childhood Rhabdomyosarcoma Treatment.

    Smooth Muscle Tumors

    Leiomyosarcoma

    There is no standard treatment for leiomyosarcoma.

    So-called Fibrohistiocytic Tumors

    Plexiform fibrohistiocytic tumor

    Treatment of plexiform fibrohistiocytic tumor may include the following:

    • Surgery to completely remove the tumor.

    Undifferentiated pleomorphic sarcoma

    There is no standard treatment for undifferentiated pleomorphic sarcoma.

    Peripheral Nervous System Tumors

    Malignant peripheral nerve sheath tumor

    The treatment of malignant peripheral nerve sheath tumor may include the following:

    • Surgery to completely remove the tumor when possible.

    It is not clear whether giving radiation therapy or chemotherapy after surgery improves the tumor's response to treatment.

    Tumors of Unknown Origin (the place where the tumor first formed is not known)

    Alveolar soft part sarcoma

    Treatment of alveolar soft part sarcoma may include the following:

    • Surgery to completely remove the tumor when possible.
    • Radiation therapy if the tumor cannot be completely removed by surgery.
    • A clinical trial of targeted therapy.

    Clear cell sarcoma of soft tissue

    Treatment of clear cell sarcoma of soft tissue may include the following:

    • Surgery to remove the tumor when possible. Radiation therapy may be given after surgery.

    Desmoplastic small round cell tumor

    There is no standard treatment for desmoplastic small round cell tumor. Treatment may include the following:

    • A combination of chemotherapy, surgery, and radiation therapy.

    Epithelioid sarcoma

    Treatment of epithelioid sarcoma may include the following:

    • Surgery to remove the tumor when possible.
    • Chemotherapy.
    • Radiation therapy.

    Perivascular epithelioid cell tumors (PEComas)

    Treatment of perivascular epithelioid cell tumors may include the following:

    • Surgery to remove the tumor.
    • A clinical trial of targeted therapy (mTOR inhibitor).

    Extrarenal (extracranial) rhabdoid tumor

    Treatment of extrarenal (extracranial) rhabdoid tumor may include the following:

    • A combination of surgery to remove the tumor when possible, chemotherapy, and radiation therapy.

    Extraskeletal myxoid chondrosarcoma

    Treatment of extraskeletal myxoid chondrosarcoma may include the following:

    • Surgery to remove the tumor when possible.
    • A clinical trial of targeted therapy.

    Primitive neuroectodermal tumor (PNET)/extraskeletal Ewing tumor

    See the PDQ summary on Ewing Sarcoma Treatment.

    1 | 2 | 3
    Next Article:

    Today on WebMD

    man holding lung xray
    What you need to know.
    stem cells
    How they work for blood cancers.
     
    woman wearing pink ribbon
    Separate fact from fiction.
    Colorectal cancer cells
    Symptoms, screening tests, and more.
     
    Jennifer Goodman Linn self-portrait
    Blog
    what is your cancer risk
    HEALTH CHECK
     
    colorectal cancer treatment advances
    Video
    breast cancer overview slideshow
    SLIDESHOW
     
    prostate cancer overview
    SLIDESHOW
    lung cancer overview slideshow
    SLIDESHOW
     
    ovarian cancer overview slideshow
    SLIDESHOW
    Actor Michael Douglas
    Article