Pheochromocytomas and extra-adrenal paragangliomas are rare tumors arising from neural crest tissue that develops into sympathetic and parasympathetic paraganglia throughout the body.
The most recent World Health Organization classification utilizes the term pheochromocytoma exclusively for tumors arising from the adrenal medulla, and the term extra-adrenal paraganglioma for similar tumors that arise from other locations.
Incidence and Mortality
The incidence of pheochromocytoma is 2...
Added text to state that abdominal metastases are rare but may occur as late as 4 years after diagnosis (cited Rejin et al. as reference 7).
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WebMD Public Information from the National Cancer Institute
February 25, 2014
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