Clear Cell Sarcoma of the Kidney
Clear cell sarcoma of the kidney is a type of kidney tumor that may spread to the lung, bone, brain, or soft tissue. When it recurs (comes back) after treatment, it often recurs in the brain.
Congenital Mesoblastic Nephroma
Congenital mesoblastic nephroma is a tumor of the kidney that is often diagnosed during the first year of life. It can usually be cured.
Ewing Sarcoma (Neuroepithelial Tumor) of the Kidney
Ewing sarcoma (neuroepithelial tumor) of the kidney is rare and usually occurs in young adults. These tumors grow and spread to other parts of the body quickly.
Desmoplastic Small Round Cell Tumor of the Kidney
Desmoplastic small round cell tumor of the kidney is a rare soft tissue sarcoma. See the PDQ summary about Childhood Soft Tissue Sarcoma Treatment for more information.
Cystic Partially Differentiated Nephroblastoma
Cystic partially differentiated nephroblastoma is a very rare type of Wilms tumor made up of cysts.
Multilocular Cystic Nephroma
Multilocular cystic nephromas are benign tumors made up of cysts. These tumors can occur in one or both kidneys. Children with this type of tumor also may have pleuropulmonary blastomas, so imaging tests of the chest are done. See the PDQ summary about Unusual Cancers of Childhood Treatment for more information.
Primary Renal Synovial Sarcoma
Primary renal synovial sarcoma is a rare tumor of the kidney and is most common in young adults. These tumors grow and spread quickly.
Anaplastic Sarcoma of the Kidney
Anaplastic sarcoma of the kidney is a rare tumor that is most common in children or adolescents younger than 15 years of age. Anaplastic sarcoma of the kidney often spreads to the lungs, liver, or bones.
Nephroblastomatosis is not cancer but may become Wilms tumor.
Sometimes, after the kidneys form in the fetus, abnormal groups of kidney cells remain in one or both kidneys. In nephroblastomatosis, these abnormal groups of cells may grow in many places inside the kidney or make a thick layer around the kidney. When these groups of abnormal cells are found in a kidney that was removed for Wilms tumor, the child has an increased risk of Wilms tumor in the other kidney. Frequent follow-up testing is important for at least 7 years after the child is treated.