It is possible that the main title of the report Progressive Symmetric Erythrokeratodermia is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.
- Darier-Gottron syndrome
- progressive symmetric erythrokeratoderma
- progressive symmetric erythrokeratodermia of Gottron
Progressive symmetric erythrokeratoderma (PSEK) is a rare genetic skin disorder characterized by well-demarcated plaques of reddened, dry, and thickened skin. These lesions are distributed symmetrically on the body and tend to slowly expand and progress over time. The severity and progression of the disorder can vary greatly from one person to another, even among members of the same family. PSEK is related and can be very similar in appearance to another rare disorder called erythrokeratodermia variabilis (EKV).
Foundation for Ichthyosis & Related Skin Types
2616 N Broad Street
Colmar, PA 18915
NIH/National Institute of Arthritis and Musculoskeletal and Skin Diseases
One AMS Circle
Bethesda, MD 20892-3675
National Registry for Ichthyosis and Related Disorders
University of Washington
Dermatology Dept. Box 356524
1959 N.E. Pacific Street
Seattle, WA 98195-6524
Genetic and Rare Diseases (GARD) Information Center
PO Box 8126
Gaithersburg, MD 20898-8126
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It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report
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Last Updated: 3/19/2013
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