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How is Shwachman-Diamond syndrome treated if you have exocrine pancreatic insufficiency?

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Your doctor may prescribe PERTs, a high-fat and high-calorie diet, and vitamins and supplements. Scientists are also working to see if stem-cell transplants will treat this genetic disease.

From: EPI Treatment: What to Expect WebMD Medical Reference

SOURCES:

National Pancreas Foundation: “Exocrine Pancreatic Insufficiency (EPI).”

Medical University of South Carolina Digestive Disease Center: “What is pancreatic insufficiency?”

Lindkvist, B. , published online November 2014. World Journal of Gastroenterology

National Organization for Rare Disorders: “Shwachman-Diamond Syndrome.”

Diabetes Association of the UK: “Exocrine Pancreatic Insufficiency.”

Pancreatic Cancer Action Network: “Pancreatic Enzymes.”

Raphael, K. , published online July 2016. Clinical and Experimental Gastroenterology

Johns Hopkins Cystic Fibrosis Center: “Pancreas/Gastrointestinal Tract.”

Olesen, S.S. , August 2011. Gastroenterology

UptoDate: “Etiology and pathogenesis of chronic pancreatitis in adultsEtiology and pathogenesis of chronic pancreatitis in adults," “Treatment of chronic pancreatitis.”

Reviewed by Brunilda Nazario on October 14, 2018

SOURCES:

National Pancreas Foundation: “Exocrine Pancreatic Insufficiency (EPI).”

Medical University of South Carolina Digestive Disease Center: “What is pancreatic insufficiency?”

Lindkvist, B. , published online November 2014. World Journal of Gastroenterology

National Organization for Rare Disorders: “Shwachman-Diamond Syndrome.”

Diabetes Association of the UK: “Exocrine Pancreatic Insufficiency.”

Pancreatic Cancer Action Network: “Pancreatic Enzymes.”

Raphael, K. , published online July 2016. Clinical and Experimental Gastroenterology

Johns Hopkins Cystic Fibrosis Center: “Pancreas/Gastrointestinal Tract.”

Olesen, S.S. , August 2011. Gastroenterology

UptoDate: “Etiology and pathogenesis of chronic pancreatitis in adultsEtiology and pathogenesis of chronic pancreatitis in adults," “Treatment of chronic pancreatitis.”

Reviewed by Brunilda Nazario on October 14, 2018

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How is chronic pancreatitis treated if you have exocrine pancreatic insufficiency?

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