Klippel-Trénaunay-Weber Syndrome

Picture of Klippel-Trénaunay-Weber Syndrome

Klippel-Trénaunay-Weber Syndrome. This is a condition in which vascular malformations, varicosities, and phlebectasia cover an entire limb or other body area. There may be associated skeletal abnormalities including macrodactyly and syndactyly. A combination of port-wine stain and vascular malformations may be present from birth. The osteohypertrophy develops during the first several years of life. These figures are the front and back views of an infant who has the beginning of the angiomatous process. At this stage, the condition appears almost like a nevus flammeus. Over time, more massive vascularization and enlargement of the limb will develop. 

Color Atlas of Pediatric Dermatology Samuel Weinberg, Neil S. Prose, Leonard Kristal Copyright 2008, 1998, 1990, 1975, by the McGraw-Hill Companies, Inc. All rights reserved.

Article: Klippel-Trenaunay Syndrome

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Sources

Sources: Color Atlas of Pediatric Dermatology
Samuel Weinberg, Neil S. Prose, Leonard Kristal
Copyright 2008, 1998, 1990, 1975, by the McGraw-Hill Companies, Inc. All rights reserved.

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