Menu

Klippel-Trénaunay-Weber Syndrome

Medically Reviewed by Sabrina Felson, MD on June 22, 2021

photo of

Klippel-Trénaunay-Weber Syndrome. This is a condition in which vascular malformations, varicosities, and phlebectasia cover an entire limb or other body area. There may be associated skeletal abnormalities including macrodactyly and syndactyly. A combination of port-wine stain and vascular malformations may be present from birth. The osteohypertrophy develops during the first several years of life. This figure is the back view of an adult who has the beginning of the angiomatous process. At this stage, the condition appears almost like a nevus flammeus. Over time, more massive vascularization and enlargement of the limb will develop. 

Color Atlas of Pediatric Dermatology
Samuel Weinberg, Neil S. Prose, Leonard Kristal
Copyright 2008, 1998, 1990, 1975, by the McGraw-Hill Companies, Inc. All rights reserved.

Article: Klippel-Trenaunay Syndrome

Slideshow: Birthmarks: Port Wine Stains to Hemangiomas  
Slideshow: Tips to Keep Baby’s Skin Healthy
Slideshow: Common Childhood Skin Problems: From Rashes to Ringworm

Show Sources

Sources: 

Photo Credit: ISM / Getty Images

Color Atlas of Pediatric Dermatology
Samuel Weinberg, Neil S. Prose, Leonard Kristal
Copyright 2008, 1998, 1990, 1975, by the McGraw-Hill Companies, Inc. All rights reserved.

© 2021 WebMD, LLC. All rights reserved. View privacy policy and trust info