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    Dandy Walker Malformation

    Important
    It is possible that the main title of the report Dandy Walker Malformation is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.

    Synonyms

    • Dandy-Walker Cyst
    • Dandy-Walker Deformity
    • Dandy-Walker Syndrome
    • DWM
    • Hydrocephalus, Internal, Dandy-Walker Type
    • Hydrocephalus, Noncommunicating, Dandy-Walker Type
    • Luschka-Magendie Foramina Atresia

    Disorder Subdivisions

    • None

    General Discussion

    Dandy-Walker malformation (DWM) is a brain malformation that occurs during embryonic development of the cerebellum and 4th ventricle. The cerebellum is the area of the brain that helps coordinate movement, and is also involved with cognition and behavior. The 4th ventricle is a space around the cerebellum that channels fluid from inside to around the outside of the brain. DWM is characterized by underdevelopment (small size and abnormal position) of the middle part of the cerebellum known as the cerebellar vermis, cystic enlargement of the 4th ventricle and enlargement of the base of the skull (posterior fossa). DWM is sometimes (20-80%) associated with hydrocephalus, in which blockage of the normal flow of spinal fluid leads to excessive amounts of fluid accumulating in and around the brain. This leads to abnormally high pressure within the skull and swelling of the head, and can lead to neurological impairment.

    Resources

    Lighthouse International
    111 E 59th St
    New York, NY 10022-1202
    Tel: (800)829-0500
    Email: info@lighthouse.org
    Internet: http://www.lighthouse.org

    National Hydrocephalus Foundation
    12413 Centralia Rd.
    Lakewood, CA 90715-1653
    USA
    Tel: (562)924-6666
    Fax: (562)924-6666
    Tel: (888)857-3434
    Email: nhf@earthlink.net
    Internet: http://www.nhfonline.org

    Hydrocephalus Association
    4340 East West Highway Ste 950
    Bethesda, MD 20814
    USA
    Tel: (301)202-3811
    Fax: (301)202-3813
    Tel: (888)598-3789
    Email: info@hydroassoc.org
    Internet: http://www.hydroassoc.org

    NIH/National Institute of Neurological Disorders and Stroke
    P.O. Box 5801
    Bethesda, MD 20824
    Tel: (301)496-5751
    Fax: (301)402-2186
    Tel: (800)352-9424
    TDD: (301)468-5981
    Internet: http://www.ninds.nih.gov/

    Dandy-Walker Syndrome Network
    5030 142nd Path West
    Apple Valley, MN 55124
    USA
    Tel: (612)423-4008

    Hydrocephalus Support Group, Inc.
    1933 Mistflower Glen Ct.
    Chesterfield, MO 63005-4236
    USA
    Tel: (636)532-8228
    Fax: (314)251-5871
    Email: hydrob@earthlink.net

    Genetic and Rare Diseases (GARD) Information Center
    PO Box 8126
    Gaithersburg, MD 20898-8126
    Tel: (301)251-4925
    Fax: (301)251-4911
    Tel: (888)205-2311
    TDD: (888)205-3223
    Internet: http://rarediseases.info.nih.gov/GARD/

    Madisons Foundation
    PO Box 241956
    Los Angeles, CA 90024
    Tel: (310)264-0826
    Fax: (310)264-4766
    Email: getinfo@madisonsfoundation.org
    Internet: http://www.madisonsfoundation.org

    Dandy-Walker Alliance, Inc.
    10325 Kensington Pkwy
    Suite 384
    Kensington, MD 20895
    Tel: (877)326-3992
    Email: comments@dandy-walker.org
    Internet: http://www.dandy-walker.org

    For a Complete Report:

    This is an abstract of a report from the National Organization for Rare Disorders (NORD). A copy of the complete report can be downloaded free from the NORD website for registered users. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational therapies (if available), and references from medical literature. For a full-text version of this topic, go to www.rarediseases.org and click on Rare Disease Database under "Rare Disease Information".

    The information provided in this report is not intended for diagnostic purposes. It is provided for informational purposes only. NORD recommends that affected individuals seek the advice or counsel of their own personal physicians.

    It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report

    This disease entry is based upon medical information available through the date at the end of the topic. Since NORD's resources are limited, it is not possible to keep every entry in the Rare Disease Database completely current and accurate. Please check with the agencies listed in the Resources section for the most current information about this disorder.

    For additional information and assistance about rare disorders, please contact the National Organization for Rare Disorders at P.O. Box 1968, Danbury, CT 06813-1968; phone (203) 744-0100; web site www.rarediseases.org or email orphan@rarediseases.org

    Last Updated: 2/12/2008
    Copyright 1986, 1989, 1991, 1994, 1995, 1999, 2007, 2008 National Organization for Rare Disorders, Inc.

    WebMD Medical Reference from the National Organization for Rare Disorders

    Last Updated: May 28, 2015
    This information is not intended to replace the advice of a doctor. Healthwise disclaims any liability for the decisions you make based on this information.

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