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    Chordoma

    Important
    It is possible that the main title of the report Chordoma is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.

    Synonyms

    • Clival Chordoma
    • Familial Chordoma
    • Intracranial Chordoma
    • Sacrococcygeal Chordoma
    • Skull Base Chordoma
    • Spinal Chordoma

    Disorder Subdivisions

    • None

    General Discussion

    Summary
    A chordoma is a rare tumor that develops in the bones of the skull and the spine. These tumors arise from the remnants of the notochord, a flexible, rod-like structure that provides support to the developing embryo. During fetal development, the notochord is replaced by the bones of the spine. Notochordal cells that persist within the spinal column may give rise to chordoma. Chordomas are slow growing tumors that cause destruction of the surrounding bone and eventually extend into the surrounding soft tissue. Sometimes chordoma spreads through the bloodstream (metastasizes) to other organs, such as the lungs, lymph nodes, liver or other bones. Although chordoma can develop at any point during life, it most commonly occurs in older adults. The symptoms associated with a chordoma depend upon the size and location of the tumor. Almost all cases of chordoma occur randomly for no apparent reason. In extremely rare cases, chordomas may develop in multiple members of the same family as a result of certain genetic risk factors (familial chordoma).

    Introduction
    Chordomas may be classified as a type of sarcoma. Sarcoma is a general term for a group of cancers that can affect bone or connective tissue - the tissues that connect, support and surround various structures and organs in the body. Although chordomas are primary bone tumors, they are sometimes classified as central nervous system tumors when they occur near the skull base.

    Resources

    American Brain Tumor Association
    8550 W. Bryn Mawr Avenue, Suite 550
    Chicago, IL 60631
    USA
    Tel: (773)577-8750
    Fax: (773)577-8738
    Tel: (800)886-2282
    Email: info@abta.org
    Internet: http://www.abta.org

    American Cancer Society, Inc.
    250 Williams NW St
    Ste 6000
    Atlanta, GA 30303
    USA
    Tel: (404)320-3333
    Tel: (800)227-2345
    TDD: (866)228-4327
    Internet: http://www.cancer.org

    National Cancer Institute
    6116 Executive Blvd Suite 300
    Bethesda, MD 20892-8322
    USA
    Tel: (301)435-3848
    Tel: (800)422-6237
    TDD: (800)332-8615
    Email: cancergovstaff@mail.nih.gov
    Internet: http://www.cancer.gov

    Brain Tumour Foundation of Canada
    620 Colborne Street
    Suite 301
    London
    Ontario, N6B 3R9
    Canada
    Tel: 5196427755
    Fax: 5196427192
    Tel: 8002655106
    Email: braintumour@braintumour.ca
    Internet: http://www.braintumour.ca

    Brain Tumour UK
    Tower House
    Latimer Park
    Chesham
    Bucks, HP5 1TU
    United Kingdom
    Tel: 08454500386
    Email: enquiries@braintumouruk.org.uk
    Internet: http://www.braintumouruk.org.uk

    Cancer Research UK
    Angel Building
    407 St John Street
    London, EC1V 4AD
    United Kingdom
    Tel: 020 7242 0200
    Fax: 02071216700
    Email: cancerhelpuk@cancer.org.uk
    Internet: http://www.cancerresearchuk.org/cancer-help/

    Rare Cancer Alliance
    1649 North Pacana Way
    Green Valley, AZ 85614
    USA
    Internet: http://www.rare-cancer.org

    Chordoma Support Group
    451 Caesar Avenue
    Oakville
    Ontario, L6J 3Z1
    Canada
    Tel: 9058450372
    Email: chordomamanagers@gmail.com
    Internet: http://www.chordomasupport.org

    Friends of Cancer Research
    1800 M Street NW
    Suite 1050 South
    Washington, DC 22202
    Tel: (202)944-6700
    Email: info@focr.org
    Internet: http://www.focr.org

    National Brain Tumor Society
    55 Chapel Street
    Suite 200
    Newton, MA 02458
    Tel: (617)924-9997
    Fax: (617)924-9998
    Tel: (800) 770-8287
    Email: info@braintumor.org
    Internet: http://www.braintumor.org

    Chordoma Foundation
    PO Box 2127
    Durham, NC 27701
    USA
    Tel: (919)809-6779
    Fax: (866)367-3910
    Tel: (888)502-6109
    Email: josh@chordoma.org
    Internet: http://www.chordoma.org

    For a Complete Report:

    This is an abstract of a report from the National Organization for Rare Disorders (NORD). A copy of the complete report can be downloaded free from the NORD website for registered users. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational therapies (if available), and references from medical literature. For a full-text version of this topic, go to www.rarediseases.org and click on Rare Disease Database under "Rare Disease Information".

    The information provided in this report is not intended for diagnostic purposes. It is provided for informational purposes only. NORD recommends that affected individuals seek the advice or counsel of their own personal physicians.

    It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report

    This disease entry is based upon medical information available through the date at the end of the topic. Since NORD's resources are limited, it is not possible to keep every entry in the Rare Disease Database completely current and accurate. Please check with the agencies listed in the Resources section for the most current information about this disorder.

    For additional information and assistance about rare disorders, please contact the National Organization for Rare Disorders at P.O. Box 1968, Danbury, CT 06813-1968; phone (203) 744-0100; web site www.rarediseases.org or email orphan@rarediseases.org

    Last Updated: 5/15/2014
    Copyright 2004, 2014 National Organization for Rare Disorders, Inc.

    WebMD Medical Reference from the National Organization for Rare Disorders

    Last Updated: May 28, 2015
    This information is not intended to replace the advice of a doctor. Healthwise disclaims any liability for the decisions you make based on this information.

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