It is possible that the main title of the report Ichthyosis, Erythrokeratolysis Hiemalis is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.
- Disorder of Cornification 19 (Erythrokeratolysis Hiemalis)
- DOC 19
- Erythrokeratolysis Hiemalis
- Keratolytic Winter Erythema
- Oudtshoorn Skin
Erythrokeratolysis hiemalis is an extremely rare form of ichthyosis that was first described in South Africa but has subsequently been identified in other countries. In such cases, a link to South Africa has been determined. The disorder is characterized by periodic attacks of red (erythematous) plaques that are distributed equally on both sides of the body. A layer of skin can be peeled from these plaques. Symptoms usually improve with age. The disorder tends to become worse with the cold weather.
Foundation for Ichthyosis & Related Skin Types
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NIH/National Institute of Arthritis and Musculoskeletal and Skin Diseases
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Bethesda, MD 20892-3675
Genetic and Rare Diseases (GARD) Information Center
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It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report
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Last Updated: 4/18/2008
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